How rare is Lance Adams syndrome?

How rare is Lance Adams syndrome?

Lance-Adams syndrome (LAS) is a rare condition in which posthypoxic myoclonus occurs days or weeks after successful cardiopulmonary resuscitation. 1-3. To date, less than 150 cases have been described in the medical literature.

What is LAS syndrome?

Abstract. Lance-Adams syndrome (LAS) is a rare complication of successful cardiopulmonary resuscitation and is often accompanied by action myoclonus. LAS is seen in patients who have undergone a cardiorespiratory arrest, later regained consciousness, and then developed myoclonus days or weeks after the event.

What is Posthypoxic myoclonus?

Post-hypoxic myoclonus (PHM) refers to myoclonus occurring after hypoxic brain injury resulting from a cardiac arrest, characterised by abrupt, irregular contractions of muscles that may be focal or generalised.

What causes Lance Adams syndrome?

Hypoxic myoclonus, also known as Lance Adams syndrome, is a rare syndrome that results from the serious brain damage caused by cerebral hypoxia that often follows cardiopulmonary resuscitation.

What are the symptoms of Lance-Adams syndrome?

Lance-Adams syndrome (LAS) is chronic post-hypoxic myoclonus that is often associated with sudden lapses in muscle tone (negative myoclonus) in the legs, causing a disabling “bouncy gait.” Given its relative rarity, there are no controlled treatment studies of LAS.

Does Lance-Adams progressive get worse?

(2) Chronic: Lance-Adams syndrome, which may start from days to weeks after arrest and progressively worsen, with or without other neurological symptoms.

Does Lance Adams progressive get worse?

Is there a treatment for myoclonus?

Treatment of myoclonus focuses on medications that may help reduce symptoms. The drug of first choice is clonazepam, a type of tranquilizer. Many of the drugs used for myoclonus, such as barbiturates, phenytoin, and primidone, are also used to treat epilepsy.

What are the symptoms of Lance Adams syndrome?